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PORPHYRIA FACTS
GAIR PROBLEMS ASSOCIATED WITH PORPHYRIA
ALOPECIA [HAIR LOSS]
s
What is alopecia that occurs in porphyria?
Alopecia is the partial or complete loss of hair.
SOURCE:
Michael Lehrer, M.D.
Department of Dermatology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++++++
What is the cause of Alopecia in porphyria?
Baldness is determined by multiple genetic factors.
Occurring most often on the scalp, alopecia usually develops gradually and may
be all over (diffuse) or patchy.
Usually baldness is not caused by a disease, but is associated with porphyria.
SOURCE:
Michael Lehrer, M.D.
Department of Dermatology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++++
Can alopecia (hair loss) take place in AIP, HCP and VP?
Regional alopecia may occur in the more severely expressed cases of AIP, HCP
and VP.
SOURCE:
NORD
++++++++++++
Spotty alopecia may occur in VP patients.
SOURCE:
Robert Johnson MD
Internal Medicine
++++++++++++
The loss of hair, known as alopecia, can present in AIP patients.
SOURCE:
Robert Johnson MD
Internal Medcine
+++++++++++++++
Does loss of hair occur in PCT?
Scarring alopecia and separation of nail plates from their beds
(photoonycholysis) can be seen in more severely affected cases.
SOURCE:
Porphyria Cutaneous Tarda
Maureen B Poh-Fitzpatrick, MD,
Professor Emerita and Special Lecturer,
Department of Dermatology,
Columbia University College of Physicians and Surgeons,
Clinical Professor of Medicine,
>Division of Dermatology,
University of Tennessee College of Medicine
eMedicine Journal
+++++++++++++++++++++++++++++++
Alopecia has been documented in HCP patients.
SOURCE:
Robert Johnson MD
Internal Medicine
+++++++++++++
Alopecia, hypertrichosis, ectropion, and anemia will often result in CEP.
SOURCE:
Dr. Poh-Fitzpatrick, professor,
Department of Dermatology
Columbia University, New York
Dermatology Times,
Jun96, Vol. 17 Issue 6, p14, 2p
++++++++++++++++++++++++++++++
Alopecia known as hair loss, is caused by iron overload.
This in itself is no big deal and may only be embarrassing to the patient, but
don't forget this minor problem for the clue to a diagnosis.
SOURCE:
Heavy Metal Toxicity
Dr. Stephen B. Edelson M.D.
The Edelson Center for
Environmental & Preventive Medicine
Atlanta, Georgia
++++++++++++++++++++++++++++++
Hair loss is caused by iron overload.
This in itself is no big deal and may only be embarrassing to the patient, but
don't forget this minor problem for the clue to a diagnosis.
SOURCE:
Heavy Metal Toxicity
Dr. Stephen B. Edelson M.D.
The Edelson Center for
Environmental & Preventive Medicine
Atlanta, Georgia
++++++++++++++
Regional alopecia may occur in the more severely expressed cases of AIP,
HCP and VP.
SOURCE:
NORD
+++++++++++
HIRSUTISM
Execessive Hair Growth in Porphyria is known as Hirsutism.
Another name for excessive hair growth is Hypertrichosis
Hirsutism is the excessive growth of hair.
SOURCE:
Maxine Mason FNP
Dermatology
+++++++++
Cosmetic treatment is available if desired for hirsutism.
Upon request, doctors may suggest methods for eliminating excess hair --
bleaching, tweezing, hot wax treatments, chemical depilatories, shaving,
electrolysis or laser hair removal.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++++++++++++++++++
When the skin is involved, as it is in all non-acute and some acute types,
symptoms from sensitivity to sunlight may include a wide variety of problems
such as excessive growth of facial hair which is called hirsutism.
SOURCE:
Evaluating Porphyrin Metabolism
Dr. Grace Ziem, MD
1996
+++++++++++++++
Common causes of hirsutism include genetics, endocrine system abnormalities,
or some medications, as well as some porphyrias.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++
Hirsutism may occur.
The lesions may be mild, i.e. erosions, bullae, skin fragility or increased hair
growth on the face.
These features are clinically indistinguishable in PCT, HCP, and VP.
SOURCE:
METABOLIC LIVER DISEASE
Neville R. Pimstone, MD
Porhyria Specialist
University of California Medical School
Davis, California
+++++++++++
Excessive facial hair is usually the most troublesome symptom of hirsutism.
SOURCE:
Hirsutism associated with acute porphyria
Sr. Sylvio DeGustavo
Dermatology
+++++++++++
Signs of masculinization, such as deepening of the voice, excessive facial hair
growth, increased muscle mass, decreased breast size, increased size of
genitals, and menstrual irregularities, may be associated with this hirsutism.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++
Hirsutism produces enlarged hair follicles, enlargement and increased
pigmentation of hair.
Excessive facial hair is usually the most troublesome symptom.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++++++++++++++++++++++++
Hirsutism is a condition marked by excesive growth of hair, especially on the
face.
SOURCE:
Robert Johnson MD
Internal Medicine
+++++++++++++
When the skin is involved, as it is in all non-acute and some acute types,
symptoms from sensitivity to sunlight may include a wide variety of problems
such facial hair.
SOURCE:
Evaluating Porphyrin Metabolism
Dr. Grace Ziem, MD
1996
++++++++++++
Is hirsutism associated with PCT?
Hirsutism in PCT can occur.
SOURCE:
The Porphyrias
The Metabolic Basis of Inherited DIsease
Kappas, Sassa et. al.
1996
++++++++++++++++++++++++++++++
Hirsutism is the excessive growth of dark, coarse body hair in women (and
children).
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++
When the skin is involved, as it is in all non-acute and some acute types,
symptoms from sensitivity to sunlight may include a wide variety of problems
facial hair growth.
SOURCE:
Evaluating Porphyrin Metabolism
Dr. Grace Ziem, MD
1996
+++++++++
Risk factors for developing hirsutism include a family history of hirsutism,
endocrine disorders, and older age.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++++
Excessive facial hair is usually the most troublesome symptom of hirsutism.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++
Hirsutism is often associated with certain types of porphyria.
SOURCE:
Robert Johnson MD
Internal Medicine
+++++++++++++
Hirsutism produces enlarged hair follicles, enlargement and increased
pigmentation of hair.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
++++++++++++
Cosmetic treatment is available if desired for the damage done by hirsutism.
SOURCE:
Robert Johnson MD
Internal Medicine
+++++++++++++
Upon request, doctors may suggest methods for eliminating excess hair --
bleaching, tweezing, hot wax treatments, chemical depilatories, shaving,
electrolysis or laser hair removal.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++
If hirsutism is due to an underlying endocrine disorder, treatment of the disorder
may resolve the excessive hair growth and other symptoms.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++
Signs of masculinization, such as deepening of the voice, excessive facial hair
growth, increased muscle mass, decreased breast size, increased size of
genitals, and menstrual irregularities, may be associated with this hirsutism.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
++++++++++++++
Hirsutism may occur in PCT.
SOURCE:
The Porphyrias
Meyer, Urs A.
Harrison's Principles of Internal Medicine,
12th ed. Mc GrawHill, 1991.
++++++++++++++++++++++++++++++
What are the risk factors for hirsutism?
Risk factors for developing hirsutism include a family history of hirsutism,
endocrine disorders, and older age.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
++++++++++++++++++++++++++++++++
Signs of masculinization, such as deepening of the voice, excessive facial hair
growth, increased muscle mass, decreased breast size, increased size of
genitals, and menstrual irregularities, may be associated with this hirsutism.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++++++++++++++++++++++
Cutaneous manifestations are dermoabrasions, superficial erosions and blister
formation after trivial mechanical trauma.
The lesions leave depigmented and pigmented scars.
Hirsutism may occur.
SOURCE:
Metabolic Disorders
Porphyrias: Clinical Manifestations, Diagnosis and Treatment
Bernardo Haddock Lobo Goulart & Samanta Teixeira Basto
++++++++++++++++++++++++++++
Eventually the Hepatoerythropoietic Porphyria (HEP) patients are severely
affected with hirsutism.
SOURCE:
Medic Handbook
+++++++++++
Cosmetic treatment is available if desired if hirsutism.
Upon request, doctors may suggest methods for eliminating excess hair --
bleaching, tweezing, hot wax treatments, chemical depilatories, shaving,
electrolysis or laser hair removal.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++++++++
When the skin is involved, as it is in all non-acute and some acute types,
symptoms from sensitivity to sunlight may include a wide variety of problems
such as excessive growth of facial hair which is called hirsutism.
SOURCE:
Evaluating Porphyrin Metabolism
Dr. Grace Ziem, MD
1996
+++++++++++++++
Common causes of hirsutism include genetics, endocrine system abnormalities,
or some medications, as well as some porphyrias.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++
Hirsutism may occur.
The lesions may be mild, i.e. erosions, bullae, skin fragility or increased hair
growth on the face.
These features are clinically indistinguishable in PCT, HCP, and VP.
SOURCE:
METABOLIC LIVER DISEASE
Neville R. Pimstone, MD
Porhyria Specialist
University of California Medical School
Davis, California
+++++++++++
Hirsutism is a condition marked by excesive growth of hair, especially on the
face.
SOURCE:
Robert Johnson MD
Internal Medicine
+++++++++++++
Hirsutism is the excessive growth of dark, coarse body hair in women (and
children).
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++
When the skin is involved, as it is in all non-acute and some acute types,
symptoms from sensitivity to sunlight may include a wide variety of problems
facial hair growth which is known as hirsutism.
SOURCE:
Evaluating Porphyrin Metabolism
Dr. Grace Ziem, MD
1996
+++++++++
Risk factors for developing hirsutism include a family history of hirsutism,
endocrine disorders, and older age.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++++
Excessive facial hair is usually the most troublesome symptom of hirsutism.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++
Hirsutism produces enlarged hair follicles, enlargement and increased
pigmentation of hair.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
++++++++++++
Cosmetic treatment is available if desired for the damage done by hirsutism.
SOURCE:
Robert Johnson MD
Internal Medicine
+++++++++++++
Upon request, doctors may suggest methods for eliminating excess hair --
bleaching, tweezing, hot wax treatments, chemical depilatories, shaving,
electrolysis or laser hair removal.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++
If hirsutism is due to an underlying endocrine disorder, treatment of the disorder
may resolve the excessive hair growth and other symptoms.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++ +++
Hirsutism means excessive hair.
Hypertrichosis is another name for hitsutism.
Excessive growth of dark, coarse body hair in women and children is known as
hirsutism.
Hirsutism is a condition in which there is excessive growth of hair on the face or
body.
Although hirsutism can occur in both men and women, it is usually only a
problem for women.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
Hirsutism produces enlarged hair follicles, enlargement and increased
pigmentation of hair, and typically occurs in a distribution pattern normally seen
in adult males.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++
Some medicines can cause excessive hair growth. These medicines include
birth control pills, hormones and anabolic steroids
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
Women with hirsutism have dark, thick hair on their face, or their chest,
abdomen and back.
This thick, dark hair is different from the hair that some women have on their
upper lip, chin, breasts or stomach, or the fine "baby" hair all over their body.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++
Excessive facial hair is usually the most troublesome symptom.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++
Common causes include endocrine system abnormalities that are associated
with some types of porphyria.
Risk factors for developing hirsutism include a family history of hirsutism or
endocrine disorders or certain types of porphyria.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++
There is cosmetic treatment is available if desired.
Depilatories, or creams that remove hair, can also be used. They leave no
stubble. However, these creams may irritate your skin.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++
Bleaching paste may also be used.
Apply the paste to your skin and let it remain for about 10 minutes.
Then remove according to the directions on the label.
Bleaching products can also irritate your skin.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
Plucking and waxing can cause skin irritation and make the hair grow faster by
increasing the blood supply to the follicle.
These methods aren't recommended.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
Upon request, doctors may suggest methods for eliminating excess hair --
bleaching, tweezing, hot wax treatments, chemical depilatories, shaving,
electrolysis or laser hair removal.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++
If hirsutism is due to an underlying endocrine disorder, treatment of the disorder
may resolve the
excessive hair growth and other symptoms.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++
Physical methods of hair removal
Bleaching
Bleaching makes the excessive hair less obvious.
Depilatory creams
Depilatory creams are generally based on thioglycolate (also used in
perming solutions). A thick layer is applied for 15-30 minutes to the hairy
area, then wiped off and the hair comes off with the cream. Depilatory
creams can irritate and cause dermatitis.
Shaving
Shaving, if necessary twice daily, will prevent unsightly stubble. Shaving
does not make the hair grow more thickly.
Waxing
Waxing needs to be repeated every six weeks. The warm wax hardens on
the skin and as it is stripped off, the hairs are pulled out with it from the
roots.
Epilady
The Epilady removes the hair by a combined cut and pull.
Electrolysis/thermolysis
Electrolysis or thermolysis may result in permanent hair loss but it takes
time. A small probe is inserted along each hair, and a small electrical or
heat discharge destroys the hair. A small area is treated every few weeks.
It can be expensive if the area affected is extensive. Unskilled treatment
may cause scarring.
Laser therapy
New long wavelength lasers are under investigation for the removal of body
hair. Time will tell how effective these will be.
Complications of physical methods of hair removal
Folliculitis is an unfortunate risk of plucking, shaving, and waxing. The
treated hair follicles become inflamed, and painful pustules may develop.
Folliculitis may take weeks to settle. Hair removal has to be stopped, at
least temporarily.
HAIR HYPERTRICHOSIS.
Common causes of hypertrichosis (excessive hair growth) include genetics,
endocrine system abnormalities, or some medications, as well as some
porphyrias.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
++++++++++++++++++++++ .
Excessive growth of dark, coarse body hair.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
+++++++++++++++++
Signs of masculinization, such as deepening of the voice, excessive facial hair
growth, increased muscle mass, decreased breast size, increased size of
genitals, and menstrual irregularities, may be associated with this hpertrichosis.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++++++++++++++++++++++
Facial hair can appear as part of skin invovlement in porphyria.
When the skin is involved, as it is in all non-acute and some acute types,
symptoms from sensitivity to sunlight may include a wide variety of problems
such as rashes, blisters, changes in skin pigment, changes in facial hair, and
fragile skin that injures more easily.
SOURCE:
Evaluating Porphyrin Metabolism
Dr. Grace Ziem, MD
1996
++++++++++++++++++++++++++++++
Common causes include genetics, endocrine system abnormalities. or well as
some forms of porphyria.
There may be excessive facial hair growth.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++++++
Hypertrichosis can follow chronic sun exposure in EPP..
SOURCE:
Dr. Robert Johnson M.D.
Retired Clinician
++++++++++++++
Signs of masculinization, such as deepening of the voice, excessive facial hair
growth,increased muscle mass, decreased breast size, increased size of
genitals, and menstrual irregularities, may be associated with this hypertrichosis.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
++++++++++++++++
In Variegate Porphyria (VP) there can be facial hypertrichosis.
SOURCE:
MEDIC'S HANDBOOK
1995
+++++++++++++++
Congenital ErythropoieticPorphyria CEP) or (Gunther'sdisease) patients can be
abnormally hairy which is called hypertrichosis.
SOURCE:
Robert Johnson M.D.
Internal Medicine
+++++++++++++++++++++++++++++
Hypertrichosis is often observed in PCT patients with most florid over temporal
and malar facial areas, but also sometimes present on arms and legs.
SOURCE:
Porphyria Cutaneous Tarda
Maureen B Poh-Fitzpatrick, MD,
Professor Emerita and Special Lecturer,
Department of Dermatology,
Columbia University College of Physicians and Surgeons,
Clinical Professor of Medicine,
Division of Dermatology,
University of Tennessee College of Medicine
eMedicine Journal
+++++++++++++++++++++++
Excessive facial or body hair growth is the symptom of hypertrichosis.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++++++++
If hirsutism is due to an underlying endocrine disorder, treatment of the disorder
may resolve the excessive hair growth and other symptoms.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
++++++++++++++++
The treatment and management of porphyria iself helps in the treatment of
hypertrichosis.
SOURCE:
Robert Johnson MD
Internal Medicine
++++++++++++++
Hypertrichosis in porphyria is an excessive growth of dark, coarse body hair.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
+++++++++++++++++++++++++++++++++
Hypertrichosis is an excesive growth of dark, coarse body hair ] in women (and
children).
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++++++++
Hypertrichosis is also called hirsutism.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
+++++++++++++++++++++++++++++++
Cosmetic treatment is available if desired.
Upon request, doctors may suggest methods for eliminating excess hair --
bleaching, tweezing, hot wax treatments, chemical depilatories, shaving,
electrolysis or laser hair removal.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
++++++++++++++++
In EPP Hypertrichosis of the face and extremities is common.
SOURCE:
Christen M Mowad, MD,
Assistant Professor,
Department of Dermatology,
Geisinger Medical Center,
Pennsylvania State College of Medicine
+++++++++++++
Hypertrichosis and erythrodontia are also common in CEP.
SOURCE:
The Porphyrias
Meyer, Urs A.
Harrison's Principles of Internal Medicine,
12th ed. Mc GrawHill, 1991
++++++++++++++++++++++++++++++++
In EPP Hypertrichosis of the face nd extremities is common.
SOURCE:
Erythropoietic porphyria (EPP)
Maureen B Poh-Fitzpatrick, MD,
Professor Emerita and Special Lecturer,
Department of Dermatology,
Columbia University College of
Physicians and Surgeons,
Clinical Professor of Medicine,
Division of Dermatology,
University of Tennessee
College of Medicine
+++++++++++++++++
Hypertrichosis may occur in expressed cases of VP.
SOURCE:
Porphyria Resources
United Medical Services
1996
++++++++++++++++++++++++++++++
Hypertrichosis may occur in expressed cases of HCP.
SOURCE:
Porphyria Resources
United Medical Services
1996
+++++++++++++++++++++++++++++++
:
Hypertrichosis may be found in PCT.
SOURCE:
Familial and sporadic porphyria cutanea
de Verneuil, H.; Aitken, G.; Nordmann, Y. :
Human Genetics
44: 145-151, 1978.
+++++++++++++++++++++++++++
Changes in hair growth may be noted in PCT.
SOURCE:
Acute porphyrias:
Diagnosis and management.
Solberg, L.A. et. al.
Mayo Clinical Proceedings
1994;69:991-995.
++++++++++++++++++++++++++++
Hypertrichosis is often observed in PCTpatients.
SOURCE:
Acute porphyrias:
Diagnosis and management.
Solberg, L.A. et. al.
Mayo Clinical Proceedings
1994;69:991-995.
++++++++++++++
In PCT Hypertricosis (hair growth) may occur.
SOURCE:
The porphyrias
The Metabolic Basis of Inherited Disease
Kappas, A. et. al.
Chapter 52, pp. 1305-66,
1991.
++++++++++++++++++++++++++++
Dominant clinical symptoms in PCT include hypertrichosis and elastosis.
SOURCE:
Journal of Skin Pharmacology and Applied Skin Physiology
1998 Nov-Dec;
11(6):321-35
"Porphyria cutanea tarda."
Ruzicka T, MD et al.
Department of Dermatology,
Heinrich Heine University,
Dusseldorf, Germany
+++++++++++++++++++++++++++
Hypertrichosis of the face and extremities is common in CEP.
SOURCE:
Erythropoietic PorphyriaJeanette Hebel Matthews, MD,
Department of Dermatology,
The Skin Surgery Center
eMedicine Journal,
May 22 2002,
Volume 3, Number 5
++++++++++++++++++++++++++++
HEP patients exhibit photosensitivity, red urine, hypertrichosis, and
characteristic serum and urine porphyrin profiles.
SOURCE:
Pediatric Dermatology
11(3): 216-21
1994
"Neurologic disease in a child with hepatoerythropoietic porphyria." .
Parsons, J. L., E. E. Sahn, et al.
++++++++++++++++++++++++
Hypertrichosis may occur in the more severely expressed cases of HCP and
VP.
SOURCE:
NORD
++++++++++++++++++++++++++++++++
Risk factors for developing hypertrichosis include a family history of
hypertrichosis, cutaneous porphyria, endocrine disorders, and older age.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
++++++++++++++++++++++++++++
Little can be done for hypertrichosis on a permanent basis.
Nair-Three-in-One cream/lotion can be applied fpr the removal of unsightly hair.
SOURCE:
Robyn LeMadeline MSN, RN
Dermatology
+++++++++++++++++++++++++++++
Cosmetic treatment is available if desired for hypertrichosis.
Upon request, doctors may suggest methods for eliminating excess hair --
bleaching, tweezing, hot wax treatments, chemical depilatories, shaving,
electrolysis or laser hair removal.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++++++++
Hypertrichosis is the Excessive growth of dark, coarse body hair ]
in women (and children).
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++++
Hypertrichosis produces enlarged hair follicles and usually darken
pigmentation.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++++
Hypertrichosis may occur in the more severely expressed cases of HCP and
VP.
SOURCE:
NORD
http://nordx.mmc.org/testcat
+++++++++++++++
Risk factors for developing hypertrichosis include a family history of
hypertrichosis, cutaneous porphyria, endocrine disorders, and older age.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++++
Hypertrichosis is also called hisutism.
SOURCE:
Medline
U.S. National Library of Medicine,
8600 Rockville Pike,
Bethesda, MD 20894
+++++++++++++
Hypertrichosis is experienced by 11% of porphyria patients.
SOURCE:
United Health Services
Medical Education Department
1999
++++++++++
There is cosmetic treatment is available if desired.
Depilatories, or creams that remove hair, can also be used. They leave no
stubble. However, these creams may irritate your skin.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++
Bleaching paste may also be used.
Apply the paste to your skin and let it remain for about 10 minutes.
Then remove according to the directions on the label.
Bleaching products can also irritate your skin.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
Plucking and waxing can cause skin irritation and make the hair grow faster by
increasing the blood supply to the follicle.
These methods aren't recommended.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
Upon request, doctors may suggest methods for eliminating excess hair --
bleaching, tweezing, hot wax treatments, chemical depilatories, shaving,
electrolysis or laser hair removal.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++
If hirsutism is due to an underlying endocrine disorder, treatment of the disorder
may resolve the
excessive hair growth and other symptoms.
SOURCE:
Stephanie Fish, M.D.
Division of Endocrinology
University of Pennsylvania Medical Center
Philadelphia, PA.
++++++++++
Physical methods of hair removal
Bleaching
Bleaching makes the excessive hair less obvious.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
Depilatory creams
Depilatory creams are generally based on thioglycolate (also used in
perming solutions).
A thick layer is applied for 15-30 minutes to the hairy area, then wiped off and
the hair comes off with the cream.
Depilatory creams can irritate and cause dermatitis.
Many porphyria patients use “Three-in-One” cream and find it beneficial.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
Shaving
Shaving, if necessary twice daily, will prevent unsightly stubble.
Shaving does not make the hair grow more thickly.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
Waxing
Waxing needs to be repeated every six weeks. The warm wax hardens on
the skin and as it is stripped off, the hairs are pulled out with it from the
roots.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
Epilady
The Epilady removes the hair by a combined cut and pull.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
Electrolysis/thermolysis
Electrolysis or thermolysis may result in permanent hair loss but it takes
time.
A small probe is inserted along each hair, and a small electrical or heat
discharge destroys the hair.
A small area is treated every few weeks.
It can be expensive if the area affected is extensive.
Unskilled treatment may cause scarring.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
Laser therapy
New long wavelength lasers are under investigation for the removal of body
hair.
Time will tell how effective these will be.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
Complications of physical methods of hair removal
Folliculitis is an unfortunate risk of plucking, shaving, and waxing. The
treated hair follicles become inflamed, and painful pustules may develop.
Folliculitis may take weeks to settle.
Hair removal has to be stopped, at least temporarily.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
If your own body hair is causing you concern, ask your family doctor,
endocrinologist or dermatologist for advice.
SOURCE:
Genevieve Adams FNP
Dermatology
+++++++++
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